A Case Report of Arrhythmogenic Right Ventricular Dysplasia Presenting Syncope Cardiovascular Research Center, Mashhad University of Medical Sciense

Document Type : Case report


1 Associate Professor of Cardiology, Mashhad University of Medical Sciences, Mashhad, Iran

2 Resident of Cardiology, Mashhad University of Medical Sciences, Mashhad, Iran


Patients with arrhythmogenic right ventricular cardiomyopathy have Ventricular Tachycardia (VT) and left bundle branch block contours with right-axis deviation and T-waves inversion in pericardial leads.
Case report
Presenting case was a 28 years old man admitted with palpitation and syncope. The electrocardiography showed Ventricular tachycardia with left bundle branch block contour and T wave inversions in V1 to V6 and incomplete right bundle branch block and T wave inversions in V1 to V3. Echocardiography revealed right ventricular (RV) dilatation. RV function was abnormal, and aneurismal formation in free wall was seen in 3D echocardiography.
Arrhythmogenic right ventricular cardiomyopathy remains as a primary diagnoses, in case of patients with ventricular tachycardia, left bundle branch block contour and T waves inversion in pericardial leads and without any history of ischemic heart disease,


1-Horimoto M, Akino M, Takeaka T, Igarashi K, Inoue H, Kawakami Y. Evolution of left ventricular involvement in
arrhythmogenic right ventricular cardiomyopathy. Cardiology 2000; 93:197-200.
2 - Libby P. Brunwalds heart disease:a textbook of cardiovascular medicine. 8th ed.
3 -Marcus FIWJ,McKenna D,Sherrill C,Basso B,Bauce DA, Bluemke H,et al.
Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the task force
criteria. Circulation 2010; 121:1533-1541.
4-Yoerger DM, Marcus F, Sherrill D , Calkins H Towbin JA, Zareba W, et al. Echocardiographic findings in patients
meeting task force criteria for arrithmogenic right ventricular dysplasia :new insights from the multidisciplinary study
of right ventricular dysplasia. J Am Coll Cardiol 2005; 45:860-865
5 - Donal E, Raynier P .Transthoracic tissue Doppler study of right ventricular regional function in a patient with an
arrithmogenic right ventricular cardiomyopathy. Heart 2004; 90:980.
6 - Herbots L, Kowalski M, Vanhaecke J, Hatle L, Sutherland GR. Characterizing abnormal regional longitundinal
function in arrithmogenic right ventricular dysplasia: the potential clinical role of ultrasonic myocardial deformation
imaging .Eur Heart J 1988; 9:1291-302.