A Case Report of Arrhythmogenic Right Ventricular Dysplasia Presenting Syncope Cardiovascular Research Center, Mashhad University of Medical Sciense

Document Type : Case report

Authors

1 Associate Professor of Cardiology, Mashhad University of Medical Sciences, Mashhad, Iran

2 Resident of Cardiology, Mashhad University of Medical Sciences, Mashhad, Iran

Abstract

Introduction
Patients with arrhythmogenic right ventricular cardiomyopathy have Ventricular Tachycardia (VT) and left bundle branch block contours with right-axis deviation and T-waves inversion in pericardial leads.
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Case report
Presenting case was a 28 years old man admitted with palpitation and syncope. The electrocardiography showed Ventricular tachycardia with left bundle branch block contour and T wave inversions in V1 to V6 and incomplete right bundle branch block and T wave inversions in V1 to V3. Echocardiography revealed right ventricular (RV) dilatation. RV function was abnormal, and aneurismal formation in free wall was seen in 3D echocardiography.
Conclusion
Arrhythmogenic right ventricular cardiomyopathy remains as a primary diagnoses, in case of patients with ventricular tachycardia, left bundle branch block contour and T waves inversion in pericardial leads and without any history of ischemic heart disease,

Keywords


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